Orphan diseases I

Thematic Poster
Chairs: Carlo Vancheri (Catania, Italy), Marlies S. Wijsenbeek (Rotterdam, Netherlands), Effrosyni D. Manali (Athens, Greece), Spyridon Papiris (Athens, Greece)

Review of care in patients dying of pulmonary fibrosis in a district general hospital Nevan Meghani (Salford, United Kingdom), Nevan Meghani, Beth Turnpenny, Abdul Ashish
Hypoxic challenge testing in idiopathic pulmonary fibrosis Ian Cliff (Stoke-On-Trent, United Kingdom), Ian Cliff, Michael Hepple, Marie Hardy, Jacqueline Piggott, Pamela Birks, Monica Spiteri, Naveed Mustfa, Helen Stone
Clinical features of patients with idiopathic pulmonary upper lobe-dominant fibrosis Shun Shinomiya (Saitama-ken, Japan), Shun Shinomiya, Yutaka Usui, Akiko Kaga, Makoto Nagta
Surfactant protein-D level as a predictor of prognosis of interstitial lung disease induced by anticancer agents in advanced lung cancer Motoyasu Kato (Bunkyo, Tokyo, Japan), Motoyasu Kato, Shinichi Sasaki, Takehito Shukuya, Yasuhito Sekimoto, Hiroaki Ihara, Ryo Koyama, Naoko Suimada, Osamu Nagashima, Fumiyuki Takahashi, Shigeru Tominaga, Kazuhisa Takahashi
Inhaled sargramostim and whole lung lavage (WLL) as therapy of autoimmune pulmonary alveolar proteinosis (aPAP) Ilaria Campo (Pavia, Italy), Ilaria Campo, Francesca Mariani, Elena Paracchini, Zamir Kadija, Michele Zorzetto, Carmine Tinelli, Giuseppe Rodi, Federica Meloni, Matthias Griese, Bruce Trapnell, Gerhard Scheuch, Bernhard Muellinger, Maurizio Luisetti
Whole lung lavage therapy (WLL) of pulmonary alveolar proteinosis (PAP): A global survey of current practices and procedures Ilaria Campo (Pavia, Italy), Ilaria Campo, Maurizio Luisetti, Matthias Griese, Bruce C. Trapnell, Francesco Bonella, Jan Grutters, Koh Nakata, Coline Van Moorsel, Ulrich Costabel, Vincent Cottin, Toshio Ichiwata, Yoshikazu Inoue, Antonio Braschi, Giacomo Bonizzoni, Giorgio Iotti, Carmine Tinelli, Giuseppe Rodi, WLL International Study Group
Short-term variation of lung function and airway inflammation in children and adolescents with bronchiolitis obliterans Martin Rosewich (Bad Homburg, Germany), Martin Rosewich, Jonas Eckrich, Felix Michel, Ralf Schubert, Stefan Zielen
Establishment of the consecutive registration system for pulmonary alveolar proteinosis in Japan: Updated incidence, prevalence and surveillance for intractable cases Yoshikazu Inoue (Osaka, Japan), Yoshikazu Inoue, Koh Nakata, Etsuro Yamaguchi, Toru Arai, Chikatoshi Sugimoto, Yasuhiro Setoguchi, Toshio Ichiwata, Masahito Ebina, Kazutoshi Cho, Ryushi Tazawa, Haruyuki Ishii, Takahiro Kasai, Masanori Akira, Kanji Uchida, Hiroshi Kida, Sakae Homma, Koichiro Tatsumi, Arata Azuma, Koichi Hagiwara, Keisuke Tomii, Masanori Kitaichi, Masaru Suzuki, Kohnosuke Morimoto, Toshinori Takada, Hideaki Nakayama, Shinya Ohkouchi, Takahiro Tanaka, Masaki Hirose, Akiko Matsumuro
Pulmonary function tests for lymphangioleiomyomatosis screening in women with tuberous sclerosis complex Silvia Terraneo (Arosio, Italy), Fabiano Di Marco, Silvia Terraneo, Giuseppina Palumbo, Gianluca Imeri, Francesca La Briola, Silvia Tresoldi, Angela Volpi, Lorenzo Gualandri, Filippo Ghelma, Rosa Maria Alfano, Emanuele Montanari, Alfredo Gorio, Elena Lesma, Angela Peron, Maria Paola Canevini, Stefano Centanni
Lymphangioma in patients with pulmonary lymphangioleiomyomatosis – Results of sirolimus treatment Elzbieta Radzikowska (Warsaw, Poland), Elzbieta Radzikowska, Katarzyna Blasinska-Przerwa, Paulina Jagus, Elzbieta Wiatr, Joanna Chorostowska-Wynimko, Kazimierz Roszkowski-Sliz
Inhaled GM-CSF in pulmonary alveolar proteinosis (PAP) patient refractory to plasmapheresis combined with multiple whole lung lavages (WLL) Ilaria Campo (Pavia, Italy), Francesca Mariani, Ilaria Campo, Elena Paracchini, Davide Piloni, Zamir Kadija, Michele Zorzetto, Annalisa De Silvestri, Carmine Tinelli, Federica Meloni, Maurizio Luisetti
Inhaled rhGM-CSF (molgramostim) in the first randomised, double-blind, placebo-controlled, international trial in patients with autoimmune alveolar proteinosis (aPAP) Francesco Bonella (Dusseldorf, Germany), Francesco Bonella, Yoshikazu Inoue, Inge Tarnow, Cecilia Ganslandt, Mette Vinge, Kim Arvid Nielsen, Cliff Morgan
Serum biomarkers as prognostic factors of autoimmune pulmonary alveolar proteinosis after whole lung lavage Chikatoshi Sugimoto (Sakai, Japan), Chikatoshi Sugimoto, Toru Arai, Akiko Matsumuro, Masaki Hirose, Youhei Kimura, Shinji Futami, Taro Koba, Shoko Sonobe, Sayoko Tokura, Keiko Nakao, Syojiro Minomo, Tomoko Kagawa, Yasushi Inoue, Yoshikazu Inoue
Family history of pneumothorax leading to Birt-Hogg-Dubé syndrome diagnosis Agisilaos Dervas (Athens, Greece), Agisilaos Dervas, Dimosthenis Papapetrou, Amerini Dimitrakopoulou, Dimitri Tchernitchko, Caroline Kannengiesser, Raphael Borie, Demosthenes Bouros, Spyros Papiris, Effrosyni Manali
Eosinophilic lung disease Samira Aouadi (Arina, Tunisia), Samira Aouadi, Boutheina Melki, Emna Braham, Houda Gharsalli, Sonia Maâlej, Leila Douik Elgharbi
Environmental exposures in 513 patients of hypersensitivity pneumonitis: Prospective ILD India registry Sheetu Singh (Jaipur, India), Sheetu Singh, Bridget Collins, Bharat Bhushen Sharma, Jyotsana M. Joshi, Deepak Talwar, Sandeep Katiyar, Nishtha Singh, Lawrence Ho, Jai Kumar Samaria, Parthasarthi Bhattacharya, Rakesh Gupta, Sudhir Chaudhari, Tejraj Singh, Vijay Moond, Sudhakar Pipavath, Jitesh Ahuja, Ravindran Chetambath, Aloke G. Ghoshal, Nirmal Kumar Jain, H.J. Gayathri Joshy, Surya Kant, Parvaiz Koul, Raja Dhar, Rajesh Swarnkar, Surendra K. Sharma, Dhrubajyoti Roy, Kripesh R. Sarmah, Bhavin Jankharia, Rodney A. Schmidt, Virendra Singh, Ganesh Raghu
Rare cause of interstitiel lung disease in children: Pleuroparanchymal fibroelastosis Nilay Baş İkizoğlu (Istanbul, Turkey), Nilay Bas Ikizoglu, Emine Atag, Ela Erdem Eralp, Yasemin Gokdemir, Gursu Kiyan, Fazilet Karakoc, Refika Ersu, Bulent Karadag
Bronchopulmonary dysplasia in children: Prediction and prevention of the mortality at first year Olga Logvinova (Kharkiv, Ukraine), Olga Logvinova, Ganna Senatorova, Alexandr Onikienko, Ekaterina Logvinova
Mycophenolate mofetil and azathioprine in chronic hypersensitivity pneumonitis Julie Morisset (Montreal, Canada), Julie Morisset, Kerri A. Johannson, Eric Vittinghoff, Brett M. Elicker, Kirk D. Jones, Bruno-Pierre Dubé, Harold R. Collard, Christopher J. Ryerson, Brett Ley